From: Immunoglobulin G4-related diseases in the head and neck: a systematic review
Head & Neck Manifestations | Site | Subsite | n | % |
---|---|---|---|---|
Total presentations | 730 | |||
Orbit | 384 | 52.6 | ||
Lacrimal Gland | 136 | 18.6 | ||
Extra Ocular Muscles | 9 | 1.2 | ||
Optic Nerve | 5 | 0.7 | ||
Salivary Glands | 162 | 22.2 | ||
Submandibular Gland | 107 | 14.7 | ||
Parotid Gland | 29 | 4.0 | ||
Sublingual Gland | 1 | 0.1 | ||
Minor Salivary Gland | 1 | 0.1 | ||
Thyroid | 31 | 4.2 | ||
Facial Skin | 6 | 0.8 | ||
Trigeminal Nerve | 1 | 0.1 | ||
Cervical Lymphadenopathy | 22 | 3.0 | ||
Non Head & Neck Manifestations | Site | n | % | |
Other Organ Involvement | 68 | 9.3 | ||
Mediastinal/Pelvic Lymphadenopathy | 56 | 7.7 |