Fig. 2

Cochlear implant performance in TMPRSS3- and control-group. A Boxplot of pure tone average (PTA) scores in the TMPRSS3-group. The pre-implantation PTA indicates the best-aided/unaided PTA measured with inserts/headphone. The follow-up PTA are free field measurements. The long-term follow up was 7.2 ± 3.7 years. B Boxplot of phoneme scores at 70 dB in the TMPRSS3-group. The pre-implantation phoneme-score indicates the best-aided/unaided phoneme score measured with inserts/headphone. The follow-up phoneme scores are free field measurements. The long-term follow up was 9.8 ± 3.7 years. C Boxplot of the long-term phoneme scores at 70 dB in the TMPRSS3-group and control-group, with a follow up time of respectively 9.8 ± 3.7 and 8.7 ± 3.2 years. D Phoneme score at 70 dB of the total study population (TMPRSS3- and control group) ranged from lowest to highest with a mean phoneme score of 85 ± 14% at a mean follow up time of 7.8 years. Black bars indicate the TMPRSS3-patients